Infantile myofibromatosis is an uncommon, benign, probably hamartomatous proliferation of myofibroblasts. This lesions are most often present before the age of 2 years, show a male predomenance and may be multiple or solitary. The solitary
lesions
arise
in the demis, subcutis, or deep soft tissue, most commonly in the head and neck region or trunk. The clinical course is benign and spontaneous regression is not infrequent. A female newborn presented with a tumorous lesion on the upper portion of
the
right eyelid. Physical examination showed a firm, non-tender, fixed, erythematous, 3×3cm sized tumor. Histologic examination revealed a spindle cell tumor in the dermis wit a whorled arrangemat and grouped fascicles. There was no evidence for
potential
visceral and bony involvement. Follow-up examination at 6 months of age revealed a remarkable degree of spontaneous involution. (Kor J Dermatol 1994 ; 32(5) : 907~910)
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